Primary sclerosing cholangitis revealed by pregnancy

Introduction: Primary sclerosing cholangitis (PSC) is a chronic cholestatic liver disease of poorly understood, probably dysimmune, mechanism. It slow-growing disease, with tendency to worsen. We are reporting rare case primary revealed during pregnancy. Case presentation: A 30-year-old woman who had pruritus 12 weeks gestation disturbance the biologic tests. Imaging investigations found areas stenosis and dilation VBIH right left hepatic bile ducts suggestive evidence portal hypertension. She was put under treatment by ursodeoxycholic acid pregnancy proceeded without maternal-fetal complications giving birth healthy newborn uneventful postpartum follow-up. Conclusion: This highlights importance considering pathologies other than benign intrahepatic cholestasis as cause